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Table 1 Diagnostic criteria for systemic sclerosis (American College of Rheumatology/European League Against Rheumatism criteria for the classification of systemic sclerosis [23])

From: Systemic sclerosis due to crystalline silica exposure among jewelry workers in Korea: two case reports

Item Sub-item(s) Weight/score a Case 1 Case 2
Skin thickening of the fingers of both hands extending proximal to the metacarpophalangeal joints (sufficient criterion)   9
Skin thickening of the fingers (only count the higher score) Puffy fingers 2
Sclerodactyly of the fingers (distal to the metacarpophalangeal joints but proximal to the proximal
interphalangeal joints)
4
Fingertip lesions (only count the higher score) Digital tip ulcers 2
Fingertip pitting scars 3
Telangiectasia   2
Abnormal nailfold capillaries   2
Pulmonary arterial hypertension and/or interstitial lung disease (maximum score is 2) Pulmonary arterial hypertension 2
Interstitial lung disease 2
Raynaud’s syndrome   3
SSc-related autoantibodies (anti-centromere, anti– topoisomerase I [anti–Scl-70], anti–RNA polymerase III) (maximum score is 3) Anti-centromere 3 N N
Anti–topoisomerase I
Anti–RNA polymerase III
  1. aThe total score is determined by adding the maximum weight (score) in each category. Patients with a total score of nine or higher are classified as having definitive scleroderma
  2. yes; no confirmation; N negative